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An unusual presentation of hypodontia confined to a mandibular quadrant

From Volume 6, Issue 4, October 2013 | Pages 109-111

Authors

Christopher S Barker

BChD, MFDS RCS(Ed)

Specialist Registrar in Orthodontics

Articles by Christopher S Barker

Jonathan R Sandy

PhD, MSc, BDS, FDS MOrth, FMedSci

Professor in Orthodontics, Department of Child Dental Health, Bristol Dental Hospital, Bristol

Articles by Jonathan R Sandy

Abstract

Treatment of patients with extensive hypodontia can present many difficulties in treatment planning for the multi-disciplinary team. Presented is an interesting case of non-syndromic hypodontia where the developmental absence of teeth is related to only one quadrant of the mouth. This unusual case of hypodontia appears to be sporadic with no familial or environmental history.

Clinical Relevance: This case report describes an unusual presentation of hypodontia and provides a report on the current knowledge of the genetics of hypodontia

Article

Hypodontia is defined as the developmental absence of one or more teeth and has a prevalence that varies between different populations and continents. A recent meta-analysis of dental agenesis reported that, in Caucasian European populations, the prevalence, excluding third molars, is 4.6% in males and 6.3% in females.1 The site of agenesis varies within the arch and is most frequently observed at the end of each dental series. The mandibular second premolar is the most commonly affected tooth (2.91–3.22%), followed by the maxillary lateral incisor (1.55–1.78%) and then the maxillary second premolar (1.39–1.61%).1 Unilateral agenesis is more frequent than bilateral agenesis of teeth and females are 1.37 times more likely to be affected than males. The developmental absence of teeth in the primary dentition, although less common than the permanent dentition, has a prevalence of 0.08–1.55%.2

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